Exhibit 99.1

ASCENDIS PHARMA A/S

INDEX TO UNAUDITED CONDENSED CONSOLIDATED INTERIM FINANCIAL STATEMENTS

	Page
Unaudited Condensed Consolidated Interim Statements of Profit or Loss and Other Comprehensive Income / (Loss) for the Three Months Ended March 31, 2018 and 2017		F-2
Unaudited Condensed Consolidated Interim Statements of Financial Position as of March 31, 2018 and December 31, 2017		F-3
Unaudited Condensed Consolidated Interim Statements of Changes in Equity at March 31, 2018 and 2017		F-4
Unaudited Condensed Consolidated Interim Cash Flow Statements for the Three Months Ended March 31, 2018 and 2017		F-5
Notes to the Unaudited Condensed Consolidated Interim Financial Statements		F-6

Unaudited Condensed Consolidated Interim Statements of Profit or Loss

and Other Comprehensive Income / (Loss) for the Three Months Ended March 31

			Consolidated
	Notes		2018			2017
			(EUR’000)
Revenue		4		28			372
Research and development costs				(30,540	)		(20,608	)
General and administrative expenses				(4,662	)		(3,325	)
Operating profit / (loss)				(35,174	)		(23,561	)
Finance income				702			130
Finance expenses				(7,010	)		(1,722	)
Profit / (loss) before tax				(41,482	)		(25,153	)
Tax on profit / (loss) for the period				107			14
Net profit / (loss) for the period				(41,375	)		(25,139	)
Other comprehensive income / (loss)
Items that may be reclassified subsequently to profit or loss:
Exchange differences on translating foreign operations				(9	)		4
Other comprehensive income / (loss) for the period, net of tax				(9	)		4
Total comprehensive income / (loss) for the period, net of tax				(41,384	)		(25,135	)
Profit / (loss) for the period attributable to owners of the Company				(41,375	)		(25,139	)
Total comprehensive income / (loss) for the period attributable to owners of the Company				(41,384	)		(25,135	)
			EUR			EUR
Basic and diluted earnings / (loss) per share				(1.07	)		(0.78	)
Number of shares used for calculation (basic and diluted)(1)				38,699,204			32,428,908

⁽¹⁾ A total of 4,657,891 warrants outstanding as of March 31, 2018 can potentially dilute earnings per share in the future, but have not been included in the calculation of diluted earnings per share because they are antidilutive for the period presented. Similarly, a total of 3,613,757 warrants outstanding as of March 31, 2017 are also considered antidilutive for the period presented and have not been included in the calculation.

F-2

Unaudited Condensed Consolidated Interim Statements of Financial Position

	Notes		March 31, 2018		December 31, 2017
			(EUR’000)
Assets
Non-current assets
Intangible assets				3,495		3,495
Property, plant and equipment				2,461		2,557
Deposits				1,112		293
				7,068		6,345
Current assets
Trade receivables				34		188
Other receivables				1,128		1,410
Prepayments				7,119		6,907
Income taxes receivable				1,067		778
Cash and cash equivalents				348,410		195,351
				357,758		204,634
Total assets				364,826		210,979
Equity and liabilities
Equity
Share capital		7		5,577		4,967
Distributable equity				341,836		182,244
Total equity				347,413		187,211
Current liabilities
Trade payables and other payables				17,413		23,768
Total liabilities				17,413		23,768
Total equity and liabilities				364,826		210,979

F-3

Unaudited Condensed Consolidated Interim Statements of Changes in Equity

			Distributable Equity
			(EUR’000)
	Share Capital		Share Premium			Foreign Currency Translation Reserve			Share-based Payment Reserve		Accumulated Deficit			Total
Equity at December 31, 2017		4,967		422,675			(14	)		22,793		(263,210	)		187,211
Loss for the period		—		—			—			—		(41,375	)		(41,375	)
Other comprehensive income / (loss), net of tax		—		—			(9	)		—		—			(9	)
Total comprehensive income / (loss)		—		—			(9	)		—		(41,375	)		(41,384	)
Share-based payment (Note 6)		—		—			—			4,679		—			4,679
Capital increase		610		209,415			—			—		—			210,025
Cost of capital increase		—		(13,118	)		—			—		—			(13,118	)
Equity at March 31, 2018		5,577		618,972			(23	)		27,472		(304,585	)		347,413
			Distributable Equity
			(EUR’000)
	Share Capital		Share Premium			Foreign Currency Translation Reserve			Share-based Payment Reserve		Accumulated Deficit			Total
Equity at December 31, 2016		4,354		298,567			(79	)		13,084		(139,313	)		176,613
Loss for the period		—					—			—		(25,139	)		(25,139	)
Other comprehensive income / (loss), net of tax		—					4			—		—			4
Total comprehensive income / (loss)		—					4			—		(25,139	)		(25,135	)
Share-based payment (Note 6)		—					—			2,705		—			2,705
Capital increase		11		633			—			—		—			644
Equity at March 31, 2017		4,365		299,200			(75	)		15,789		(164,452	)		154,827

F-4

Unaudited Condensed Consolidated Interim Cash Flow Statements for the

Three Months Ended March 31

		Consolidated
	Notes	2018			2017
		(EUR’000)
Operating activities
Net profit / (loss) for the period			(41,375	)		(25,139	)
Reversal of finance income			(702	)		(130	)
Reversal of finance expenses			7,010			1,722
Reversal of tax charge			(107	)		(14	)
Adjustments for:
Share-based payment			4,679			2,705
Depreciation and amortization			198			169
Changes in working capital:
Deposits			(819	)		1
Trade receivables			154			(91	)
Other receivables			282			(1,281	)
Prepayments			(211	)		(3,662	)
Trade payables and other payables			(6,364	)		4,419
Deferred income			—			—
Cash flows generated from / (used in) operations			(37,255	)		(21,301	)
Finance income received			702			130
Finance expenses paid			(4	)		(25	)
Income taxes received / (paid)			(183	)		(54	)
Cash flows from / (used in) operating activities			(36,740	)		(21,250	)
Investing activities
Acquisition of property, plant and equipment			(102	)		(377	)
Cash flows used in investing activities			(102	)		(377	)
Financing activities
Capital increase			210,025			644
Cost of capital increase			(13,118	)		—
Cash flows from / (used in) financing activities			196,907			644
Increase / (decrease) in cash and cash equivalents			160,065			(20,983	)
Cash and cash equivalents at January 1			195,351			180,329
Effect of exchange rate changes on balances held in foreign currencies			(7,006	)		(1,698	)
Cash and cash equivalents at March 31			348,410			157,648
Restricted cash included in cash and cash equivalents			5,142			63

F-5

Notes to the Unaudited Condensed Consolidated Interim Financial Statements

Note 1—General Information

Ascendis Pharma A/S, together with its subsidiaries, is a biopharmaceutical company applying its innovative TransCon technology to build a leading, fully integrated rare disease company. Ascendis Pharma A/S was incorporated in 2006 and is headquartered in Hellerup, Denmark. Unless the context otherwise requires, references to the “Company,” “we,” “us” and “our” refer to Ascendis Pharma A/S and its subsidiaries.

The address of the Company’s registered office is Tuborg Boulevard 5, DK-2900, Hellerup, Denmark.

On February 2, 2015, the Company completed an initial public offering, or IPO, which resulted in the listing of American Depositary Shares, or ADSs, representing the Company’s ordinary shares, under the symbol “ASND” in the United States on The Nasdaq Global Select Market.

The Company’s Board of Directors approved these unaudited condensed consolidated interim financial statements on May 30, 2018.

Note 2—Summary of Significant Accounting Policies

Basis of Preparation

The unaudited condensed consolidated interim financial statements of the Company are prepared in accordance with International Accounting Standard 34, “Interim Financial Reporting”. Certain information and disclosures normally included in the consolidated financial statements prepared in accordance with International Financial Reporting Standards (“IFRS”) have been condensed or omitted. Accordingly, these condensed consolidated interim financial statements should be read in conjunction with the Company’s annual consolidated financial statements for the year ended December 31, 2017 and accompanying notes, which have been prepared in accordance with IFRS as issued by the International Accounting Standards Board, and as adopted by the European Union.

The preparation of financial statements in conformity with IFRS requires the use of certain critical accounting estimates and requires management to exercise its judgment in the process of applying the Company’s accounting policies. The areas involving a higher degree of judgment or complexity, or areas where assumptions and estimates are significant to the condensed consolidated interim financial statements are disclosed in Note 3.

Changes in Accounting Policies

As of January 1, 2018, the Company has adopted IFRS 9, “Financial Instruments”, which introduces a new impairment model for financial assets measured at amortized cost based on an expected credit loss model, which currently applies to the Company’s bank deposits and trade receivables. The adoption of IFRS 9 had no material impact on the Company’s financial reporting. Further, the Company has adopted IFRS 15, “Revenue from Contracts with Customers”, which establishes a single, comprehensive framework for revenue recognition, based on a five-step model, which applies to the Company’s licensing agreements with multiple activities. IFRS 15 was adopted using the ‘retrospective method with the cumulative effect of initially applying this standard recognized at the date of the initial application’. The adoption of IFRS 15 had no impact on the Company’s financial reporting.

Except for the adoption of these two new standards, the accounting policies applied when preparing these condensed consolidated interim financial statements have been applied consistently to all the periods presented, unless otherwise stated and are consistent with those of the Company’s most recent annual consolidated financial statements. A description of our accounting policies is provided in the Accounting Policies section of the audited consolidated financial statements as of and for the year ended December 31, 2017.

Note 3—Critical Accounting Judgments and Key Sources of Estimation Uncertainty

In the application of our accounting policies, we are required to make judgments, estimates and assumptions about the carrying amounts of assets and liabilities that are not readily apparent from other sources. The estimates and associated assumptions are based on historical experience and other factors that are considered to be relevant. Actual results may differ from these estimates.

The estimates and underlying assumptions are reviewed on an ongoing basis. Revisions to accounting estimates are recognized in the period in which the estimate is revised if the revision affects only that period, or in the period of the revision and future periods if the revision affects both current and future periods.

F-6

Notes to the Unaudited Condensed Consolidated Interim Financial Statements

Critical judgments made in the process of applying our accounting policies and that have the most significant effect on the amounts recognized in our unaudited condensed consolidated financial statements relate to revenue recognition, share-based payment, internally generated intangible assets, and joint arrangements / collaboration agreements.

The key sources of estimation uncertainty that have a significant risk of causing a material adjustment to the carrying amount of assets and liabilities within the next financial year relate to impairment of goodwill and to recognition of accruals for manufacturing and clinical trial activities. There have been no changes to the application of significant accounting estimates, and no impairment losses have been recognized during the first three months of 2018 or 2017.

The unaudited condensed consolidated interim financial statements do not include all disclosures for critical accounting estimates and judgments that are required in the annual consolidated financial statements, and should be read in conjunction with the Company’s annual consolidated financial statements for the year ended December 31, 2017.

Note 4—Revenue

	Consolidated
	Three Months Ended March 31,
	2018		2017
	(EUR’000)
Revenue from the rendering of services		28		372
License income		—		—
Total revenue		28		372
Revenue from external customers (geographical)
USA		28		372
Total revenue		28		372

Note 5—Segment Information

We are managed and operated as one business unit. No separate business areas or separate business units have been identified in relation to product candidates or geographical markets. Accordingly, we do not disclose information on business segments or geographical markets, except for the geographical information on revenue included in Note 4.

Note 6—Warrants and Share-based Payment

Share-based payment

Ascendis Pharma A/S has established warrant programs, equity-settled share-based payment transactions, as an incentive for all of our employees, members of our Board of Directors and select external consultants.

Warrants are granted by our Board of Directors in accordance with authorizations given to it by the shareholders of Ascendis Pharma A/S. As of March 31, 2018, 6,487,812 warrants had been granted, of which 19,580 warrants have been cancelled, 1,600,845 warrants have been exercised, 2,168 warrants have expired without being exercised, and 207,328 warrants have been forfeited. As of March 31, 2018, our Board of Directors was authorized to grant up to 1,531,592 additional warrants to our employees, board members and select consultants without pre-emptive subscription rights for the shareholders of Ascendis Pharma A/S. Each warrant carries the right to subscribe for one ordinary share of a nominal value of DKK 1. The exercise price is fixed at the fair market value of our ordinary shares at the time of grant as determined by our Board of Directors. The exercise prices of outstanding warrants under our warrant programs range from €6.48 to €54.10 depending on the grant dates. Vested warrants may be exercised in two or four annual exercise periods. Apart from exercise prices and exercise periods, the programs are similar.

F-7

Notes to the Unaudited Condensed Consolidated Interim Financial Statements

Warrant Activity

The following table specifies the warrant activity during the three months ended March 31, 2018:

	Total Warrants			Weighted Average Exercise Price EUR
Outstanding at December 31, 2017		4,621,154			17.62
Granted during the period		47,000			42.85
Exercised during the period		—			—
Forfeited during the period		(10,263	)		24.25
Expired during the period		—			—
Outstanding at March 31, 2018		4,657,891			17.86
Vested at the balance sheet date		2,298,231			12.38

Warrant Compensation Costs

Warrant compensation costs are determined with basis in the grant date fair value of the warrants granted and recognized over the vesting period.

	Consolidated
	Three months Ended March 31,
	2018		2017
	(EUR’000)
Research and development costs		2,386		1,289
General and administrative expenses		2,293		1,416
Total warrant compensation costs		4,679		2,705

Note 7—Share Capital

The share capital of Ascendis Pharma A/S consists of 41,523,765 shares at a nominal value of DKK 1, all in the same share class.

On February 26, 2018, the Company completed the sale and issuance of 4,539,473 ADSs in a public offering, increasing the Company’s share capital from 36,984,292 shares to 41,523,765 shares.

Note 8—Subsequent Events

No events have occurred after the balance sheet date that would have a significant impact on the results or financial position of the Company.

F-8